Malformación arteriovenosa asociada enmascara un ganglioglioma anaplásico multifocal en un adolescente
Palabras clave:
Tumor cerebral, Niño, Hipertensión endocraneana, Ganglioglioma, CefaleaResumen
El ganglioglioma anaplásico grado III es un tumor del sistema nervioso central (SNC) agresivo, infrecuente y radiosensible. Afecta más a hombres en una relación 1,3 a 1. Su pico de incidencia se encuentra en la tercera década de la vida. Existen solo 10 casos registrados en niños en Colombia desde el 2000 al 2014, con desenlace fatal a pesar de la radioterapia. Se presenta un caso de un adolescente que debutó con cefalea con signos de alarma asociado a una malformación arteriovenosa que dificultó el diagnóstico de este raro tumor, cuya presentación fue la más agresiva: la forma multicéntrica. El conocer las manifestaciones clínicas de lesiones intracraneales ocupantes de espacio facilita la evaluación y tratamiento a los niños afectados.
Biografía del autor/a
Gustavo Adolfo Carvajal-Barrios, Universidad el Bosque
Physician, pediatrics resident, Universidad el Bosque, Bogotá D. C, Colombia
Jimena Ortiz, Hospital Militar Central
Neuroradiologist, professor ad honorem, Universidad Militar Nueva Granada (UMNG)-Hospital Militar Central (HMC), Bogotá D.C, Colombia
Natalia González, Hospital Militar Central
Pediatric hematologist/oncologist, HMC-HMC, Bogotá D. C, Colombia
José Arias, Hospital Militar Central
Pathologist, HMC. Professor ad honorem UMNG-HMC, Bogotá D. C, Colombia
Fernando Velandia, Universidad del Rosario
Neuropathologist, Senior professor, Neuroscience Group, Universidad del Rosario, Bogotá D. C, Colombia
Pilar Guerrero, Hospital Militar Central
Pediatric neurologist, associate professor of pediatric neurology, UMNG-HMC, Bogotá D. C, Colombia
Eugenia Espinosa, Hospital Militar Central
Pediatric neurologist, tenured profesor in pediatric neurology UMNG-HMC, Coordinator of graduate studies in pediatric
neurology UMNG-HMC, Bogotá D. C, Colombia
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